A macrodistrofia lipomatosa é uma entidade rara, principalmente diagnosticada em crianças, e pouquíssimo relatada em adultos. Descrevemos os achados de radiografia e tomografia computadorizada em um caso de macrodistrofia lipomatosa em uma mulher idosa que apresentava um segundo dedo do pé aumentado desde o nascimento e crescimentos ósseos que causavam efeitos de pressão e problemas cosméticos.

Macrodistrofia lipomatosa; Macrodactilia; Tomografia computadorizada

Autoria

Rajesh Sharma Mailing address: Rajesh Sharma, MD. 175 B, Ram Vihar, Janipur, Jammu, Jammu and Kashmir, India. E-mail: drrajeshradiology@gmail.com

Department of Radio-diagnosis and Imaging, Acharya Shri Chander College of Medical Sciences Hospital, Sidhra, Jammu, Jammu and Kashmir, IndiaAcharya Shri Chander College of Medical Sciences HospitalIndiaSidhra, Jammu, Jammu and Kashmir, IndiaDepartment of Radio-diagnosis and Imaging, Acharya Shri Chander College of Medical Sciences Hospital, Sidhra, Jammu, Jammu and Kashmir, India

Puneet Gupta

Manik Mahajan

Manjit Arora

Anchal Gupta

Mailing address: Rajesh Sharma, MD. 175 B, Ram Vihar, Janipur, Jammu, Jammu and Kashmir, India. E-mail: drrajeshradiology@gmail.com

SCIMAGO INSTITUTIONS RANKINGS

Figuras

Figuras (3)

Thumbnail

Figure 1
Photograph of the right foot, showing an enlarged second toe and a palpable hard bony lump on its medial aspect.

Thumbnail

Figure 2
Plain radiographs, in the anteroposterior and oblique planes (A and B, respectively), of the right foot, showing marked hypertrophy of the second toe with associated enlargement of the soft tissue and phalanges; near complete obliteration of metacarpophalangeal, proximal interphalangeal, and distal interphalangeal joint spaces; and dense bony outgrowths at the medial end of the proximal and distal interphalangeal joints. Note also the thickened, sclerotic cortex of the proximal phalanx of the second toe.

Thumbnail

Figure 3
A: Non-contrast-enhanced CT scan, in the axial plane, showing marked soft-tissue hypertrophy containing abnormal hypodense areas of fat attenuation involving the second toe of the right foot. B: Non-contrast-enhanced CT scan, in the axial plane, showing the thickened, sclerotic proximal phalanx of the second toe, with an accentuated trabecular pattern (arrow). C,D: Non-contrast-enhanced sagittal CT reconstruction, showing fusion of the proximal and distal interphalangeal joints (white arrows), with small bony protuberances arising from the medial end of the joints (gray arrows).

Figure 1 Photograph of the right foot, showing an enlarged second toe and a palpable hard bony lump on its medial aspect.

Figure 2 Plain radiographs, in the anteroposterior and oblique planes (A and B, respectively), of the right foot, showing marked hypertrophy of the second toe with associated enlargement of the soft tissue and phalanges; near complete obliteration of metacarpophalangeal, proximal interphalangeal, and distal interphalangeal joint spaces; and dense bony outgrowths at the medial end of the proximal and distal interphalangeal joints. Note also the thickened, sclerotic cortex of the proximal phalanx of the second toe.

Figure 3 A: Non-contrast-enhanced CT scan, in the axial plane, showing marked soft-tissue hypertrophy containing abnormal hypodense areas of fat attenuation involving the second toe of the right foot. B: Non-contrast-enhanced CT scan, in the axial plane, showing the thickened, sclerotic proximal phalanx of the second toe, with an accentuated trabecular pattern (arrow). C,D: Non-contrast-enhanced sagittal CT reconstruction, showing fusion of the proximal and distal interphalangeal joints (white arrows), with small bony protuberances arising from the medial end of the joints (gray arrows).

Como citar

copiar

Publicação do Colégio Brasileiro de Radiologia e Diagnóstico por Imagem Av. Paulista, 37 - 7º andar - conjunto 71, 01311-902 - São Paulo - SP, Tel.: +55 11 3372-4541, Fax: 3285-1690, Fax: +55 11 3285-1690 - São Paulo - SP - Brazil
E-mail: radiologiabrasileira@cbr.org.br

Acompanhe os números deste periódico no seu leitor de RSS

Versão para download de PDF

PDF

Inglês

Versões e tradução automática

Versão original do texto

English

Tradução automática

Google Translator
Microsoft Translator

Como citar

RIS

BIBTEX

Outros formatos de citação e exportação:

SciELO - Scientific Electronic Library Online
Rua Dr. Diogo de Faria, 1087 – 9º andar – Vila Clementino 04037-003 São Paulo/SP - Brasil
E-mail: scielo@scielo.org

Leia a Declaração de Acesso Aberto

Métricas

Mensagem

[1] Mailing address: Rajesh Sharma, MD. 175 B, Ram Vihar, Janipur, Jammu, Jammu and Kashmir, India. E-mail: drrajeshradiology@gmail.com