ABSTRACT
Introduction:
The angiomyolipoma (AML) is constituted by adipose tissue, blood vessels and smooth muscle fiber; follows a benign clinical course, with slow growth and absence of metastasis, occurring in tuberous sclerosis or sporadically.
Objective:
We intend to describe the clinical, radiological and histological aspects of this tumor.
Case report:
A-64-year-old woman presented with abdominal pain and dyspepsia. Tomography showed hepatic, renal and mesenteric nodules. Histological evaluation of mesenteric lymph node revealed perivascular epithelioid differentiation neoplasia, compatible with AML/perivascular epithelioid cell tumor (PEComa), positive for anti-S100, anti-human melanoma black-45 (HMB-45) and anti-smooth muscle actin.
Conclusion:
We described a rare AML with renal, hepatic and lymph node involvement, representing a multicenter version instead of metastasis.
Key words:
angiomyolipoma; tuberous sclerosis; perivascular epithelioid cell neoplasms
CT: computed tomography.
HE: hematoxylin and eosin.
HE: hematoxylin and eosin.
HMB-45: human melanoma black-45.