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McCune Albright syndrome - diffuse orbital involvement due to fibrous dysplasia: a case report

Fibrous dysplasia is a benign, slowly progressive bone disorder, in which normal bone is replaced by fibrous tissue. It is called McCune Albright syndrome when associated with skin hyperpigmentation and endocrinological disorders. We report a rare case of McCune Albright syndrome in a boy, who presented bilateral and diffuse involvement of orbits but few external craniofacial distortions.

Fibrous dysplasia, polyostotic; Orbital diseases; Craniofacial abnormalities; Facial bones


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