Acessibilidade / Reportar erro

Albopapuloid epidermolysis bullosa (Pasini's variant)

Albopapuloid epidermolysis bullosa (Pasini's variant) is a rare, autosomal dominant inherited disorder. The authors report the case of a 37-year-old female patient with blisters on trauma areas, atrophic macules (albopapuloid lesions) and milia, with onset of disease at age seven. The histopathological exam of the blister reveals a subepidermal cleavage.

epidermolysis bullosa; epidermolysis bullosa dystrophica


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